Table 1

Pulmonary artery (PA) anomalies in del22q and non-del22q patients

Anomaly22q11 deletion (n = 25)No 22q11 deletion (n = 69)
Absent confluent central PA 3/25 (12%)3/69 (4%)
Absent pulmonary trunk (in patients without MAPCA) 1/15 (6%)9/66 (13.5%)
MAPCA10/25 (40%)3/69 (4.4%)1-150
  • 1-150 p < 0.001.

  • MAPCA, major aortopulmonary collateral arteries.