Table 2

Study protocol

Before PTSMA After PTSMA 3 months after PTSMA 12 months after PTSMA and yearly thereafter
HistoryHistoryHistoryHistory
Clinical statusClinical statusClinical statusClinical status
ECGECGECGECG
Lung function testEnzyme monitoring
Bicycle stress testBicycle stress testBicycle stress test
Pulmonary artery catheterPulmonary artery catheter
EchocardiographyEchocardiographyEchocardiographyEchocardiography
Diagnostic cardiac catheterisation (Diagnostic cardiac ‚ÄÉcatheterisation)