Patients with congenital long QT syndrome and documented torsade de pointes reported in the literature
| Patients reported in our original series2 | Patients reported by others1-151 3 6 13-50 62 63 | All patients | |
| Number of patients. | 15 | 47 | 62 |
| Age (SD)1-152 in years | 28 (19)1-150 | 18 (16)1-153 | 21(17) |
| Infants (⩽3 years old) | 1 (7%) | 9 (21%)1-153 | 10 (19%) |
| Females | 12 (80%) | 28 (72%)1-153 | 40 (74%) |
| Deafness | 0 | 6 (15%)1-153 | 6 (11%) |
| Mean (SD) QTc (ms) | 589 (85) | 575 (82) | 579 (75) |
| QT score77(range) | 5.2 (4–6.5) | 5.5 (4–6.5) | 5.6 (4–6.5) |
| No β blocker treatment1-152 | 13 (87%) | 33 (76%)1-153 | 46 (79%) |
| Pause dependent TdP | 14 (93%) | 32 (68%) | 46 (74%) |
↵1-150 p < 0.05 when comparing the results in our series with those published by others.
↵1-151 Including one patient reported by us3 after publication of our original series.2
↵1-152 At the time of arrhythmia documentation.
↵1-153 Data on age, sex, history of deafness and number of patients receiving treatment at the time of arrhythmia documentation was not available for 5, 6, 7 and 4 patients published by others, respectively.