Table 2

Morphometric and haemodynamic variables in normotensive Williams patients and controls

Variable Normotensive Williams patients (n=12) Controls
(n=21)
p Value
Intima–media thickness (mm)0.61 (0.08)0.51 (0.02)< 0.001
Diastolic diameter (mm)4.1 (0.4)5.1 (0.6)< 0.001
IMT/diastolic diameter0.15 (0.02)0.10 (0.01)< 0.001
Distensibility (mm Hg−1.10−2)1.1 (0.3)0.8 (0.3)< 0.01
Cross sectional compliance (mm2.mm Hg−1)0.14 (0.04)0.15 (0.05)NS
Circumferential wall stress (mm Hg.102)2.1 (0.5)3.0 (0.7)< 0.01
Young's elastic modulus (Einc) (mm Hg.102)7.4 (2.0)14.0 (5.0)< 0.001
  • Values are mean (SD).

  • IMT, intima–media thickness.