Table 1

Significance classification system currently in use in the paediatric cardiology database

C Complex—absent or hypoplastic chamber or valve or common valve: includes complete atrioventricular septal defect (CAVSD), hypoplastic left heart syndrome (HLHS), pulmonary atresias, tricuspid atresias, truncus arteriosus, double inlet left ventricle (DILV), mitral atresia, aortic atresia, congenitally corrected transposition of the great arteries (CTGA)
S Significant—congenital heart disease requiring operation or intervention but not included in complex group: includes aortopulmonary window, critical aortic stenosis, partial AVSD, coarctation, ventricular septal defect (requiring operation), transposition of the great arteries (TGA), tetralogy of Fallot, total anomalous pulmonary venous connection (excludes persistent arterial duct, atrial septal defect)
M Minor—no intervention: 4 chambers, 4 valves—includes mainly small ventricular septal defect (VSD), less severe aortic stenosis, and pulmonary stenosis
Q Acquired: includes Kawasaki disease, Marfan's syndrome
O Normal: used only in conjunction with Down's syndrome
R Isolated arrhythmia
D Isolated duct: persistent—not preterm
P Cardiomyopathies
F ASD: no operation yet
A ASD: after ASD operation
B Bicuspid aortic valve
N Isolated arterial duct: preterm
H Duct requiring operation + minor heart malformation
X Dextrocardia, where no other abnormality
T Cardiac tumours
  • NORCAS, 1999.