Table 1

Clinical characteristics and echocardiographic findings in 15 patients with arrhythmogenic right ventricular cardiomyopathy

Case		Age (years)/ sex		Clinical presentation		Time from first symptom		ECG		SAECG		RV biopsy	RV dilatation A/T	RV WM score A/T	TAM ⩽ 20 mm, M mode	TAM E:A ⩽ 1, tissue Doppler
Case		Age (years)/ sex		Clinical presentation		Time from first symptom		Negative T waves	E wave	SAECG		RV biopsy	RV dilatation A/T	RV WM score A/T	TAM ⩽ 20 mm, M mode	TAM E:A ⩽ 1, tissue Doppler
1	58/F	VT	7 years	V1–V2	–	–	Fat, fibrosis	2/3	5/11	–	+
2	53/M	VT	16 years	V1–V5	+	+	Fat, fibrosis	2/3	8/9	+	+
3	49/M	VT	16 years	V1–V3	–	+	Fat, fibrosis	3/3	10/10	+	+
4	47/M	VT	11 years	V1–V3	–	+	Fat, fibrosis	3/3	9/9	+	+
5	45/F	Syncope	6 years	V1–V4	–	–	Fat, fibrosis	0/3	0/8	–	+
6	39/M	SVT	2 years	V1–V2	–	+	Fat, fibrosis	0/3	0/8	–	–
7	35/F	ECG abnormality	6 years	V1–V5	+	ND	ND	3/3	10/11	+	+
8	30/F	Family history	Asymptomatic	V1–V3	–	–	Fat, fibrosis	1/3	5/10	–	–
9	28/M	VT	16 years	IRBBB	–	+	Fat, fibrosis	1/3	5/10	–	+
10	23/M	Family history	Asymptomatic	V1	–	+	Fibrosis	0/3	0/10	–	+

11	22/F	Family history	Asymptomatic	V1–V3	–	–	Fat, fibrosis	2/3	1/10	–	–
12	27/M	Family history	Asymptomatic	V1–V2	–	–	Fat, fibrosis	0/3	3/10	–	+
13	59/M	VT	9 years	V1–V4	–	+	Fat, fibrosis	3/3	9/9	+	+
14	48/M	VT	10 years	V1–V6	+	+	Fat, fibrosis	3/3	12/12	+	–
15	30/M	VT	< 1 year	V1–V5	–	–	Fat, fibrosis	2/3	7/9	–	+

A, number of abnormal dimensions or wall motion score in the individual patient; E, epsilon; E:A, early to late diastolic ratio; F, female; IRBBB, incomplete right bundle branch block; M, male; ND, not done; RV, right ventricular; SAECG, signal average ECG; SVT, supraventricular tachycardia; T, total number of measured dimensions or segments; TAM, tricuspid annular motion at lateral position; VT, ventricular tachycardia, WM, wall motion.