Quinone analogs prevent enzymes targeted in Friedreich ataxia from iron-induced injury in vitro

Biofactors. 1999;9(2-4):247-51. doi: 10.1002/biof.5520090220.
No abstract available

MeSH terms

  • Aconitate Hydratase / drug effects*
  • Aconitate Hydratase / metabolism
  • Benzoquinones / pharmacology
  • Coenzymes
  • Deferoxamine / pharmacology
  • Electron Transport Complex II
  • Friedreich Ataxia / enzymology*
  • Humans
  • Iron / antagonists & inhibitors
  • Iron / toxicity*
  • Iron-Sulfur Proteins / deficiency
  • Iron-Sulfur Proteins / drug effects*
  • Iron-Sulfur Proteins / metabolism
  • Multienzyme Complexes / drug effects*
  • Multienzyme Complexes / metabolism
  • Oxidoreductases / drug effects*
  • Oxidoreductases / metabolism
  • Quinones / pharmacology*
  • Succinate Dehydrogenase / drug effects*
  • Succinate Dehydrogenase / metabolism
  • Ubiquinone / analogs & derivatives
  • Ubiquinone / pharmacology

Substances

  • Benzoquinones
  • Coenzymes
  • Iron-Sulfur Proteins
  • Multienzyme Complexes
  • Quinones
  • Ubiquinone
  • Iron
  • Oxidoreductases
  • Electron Transport Complex II
  • Succinate Dehydrogenase
  • Aconitate Hydratase
  • coenzyme Q10
  • idebenone
  • Deferoxamine