Significance of late ventricular potentials in myotonic dystrophy

Am J Cardiol. 1999 Nov 1;84(9):1099-101, A10. doi: 10.1016/s0002-9149(99)00510-x.

Abstract

In 39 patients with myotonic dystrophy, we found a high percentage of infrahissian cardiac conduction abnormalities (51%) and late potentials (46%), whereas spontaneous and inducible ventricular arrhythmias were rare. These results suggest that the prolongation of QRSD and the duration of the low-amplitude signal on the signal-averaged electrocardiogram were related to delayed activation of the His and Purkinje tissue rather than true late potentials.

MeSH terms

  • Adult
  • Atrioventricular Node / physiopathology
  • Bundle of His / physiopathology
  • Cardiac Complexes, Premature / physiopathology
  • Electrocardiography*
  • Electrocardiography, Ambulatory
  • Female
  • Heart Block / diagnosis
  • Heart Block / physiopathology
  • Heart Ventricles / physiopathology*
  • Humans
  • Male
  • Middle Aged
  • Myotonic Dystrophy / diagnosis
  • Myotonic Dystrophy / physiopathology*
  • Purkinje Fibers / physiopathology
  • Risk Factors
  • Signal Processing, Computer-Assisted*