Cardiac transplantation in Becker muscular dystrophy

Neuromuscul Disord. 1992;2(3):165-7. doi: 10.1016/0960-8966(92)90002-n.

Abstract

Becker muscular dystrophy is associated with abnormal cardiac features in about 75% of cases; up to one-third will develop ventricular dilatation leading to congestive cardiac failure. As this form of muscular dystrophy is relatively benign, failure to respond to medical treatment warrants assessment for cardiac transplantation.

Publication types

  • Review

MeSH terms

  • Heart Diseases / complications
  • Heart Diseases / therapy*
  • Heart Transplantation*
  • Humans
  • Muscular Dystrophies / complications*