Supraventricular tachyarrhythmias, congenital heart disease, and sudden cardiac death

Pediatr Cardiol. 1992 Apr;13(2):116-8. doi: 10.1007/BF00798219.

Abstract

The etiologies of sudden cardiac death following the surgical treatment of congenital heart defects remain uncertain. A young patient with prior repair of partial anomalous pulmonary venous return is presented, in whom brief episodes of a supraventricular tachyarrhythmia (rate 170/min) were documented to result in ventricular fibrillation. This unusual sequence may represent a basis for unexplained sudden cardiac death in other patients following atrial surgical procedures for the treatment of congenital heart disease.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Death, Sudden / pathology*
  • Electrocardiography, Ambulatory
  • Heart Defects, Congenital / pathology
  • Heart Defects, Congenital / surgery*
  • Heart Ventricles / pathology
  • Humans
  • Male
  • Postoperative Complications / pathology*
  • Pulmonary Veins / abnormalities*
  • Pulmonary Veins / pathology
  • Tachycardia, Supraventricular / pathology*
  • Ventricular Fibrillation / pathology