Thoracic aortopathy in Turner syndrome and the influence of bicuspid aortic valves and blood pressure: a CMR study

J Cardiovasc Magn Reson. 2010 Mar 11;12(1):12. doi: 10.1186/1532-429X-12-12.

Abstract

Background: To investigate aortic dimensions in women with Turner syndrome (TS) in relation to aortic valve morphology, blood pressure, karyotype, and clinical characteristics.

Methods and results: A cross sectional study of 102 women with TS (mean age 37.7; 18-62 years) examined by cardiovascular magnetic resonance (CMR- successful in 95), echocardiography, and 24-hour ambulatory blood pressure. Aortic diameters were measured by CMR at 8 positions along the thoracic aorta. Twenty-four healthy females were recruited as controls. In TS, aortic dilatation was present at one or more positions in 22 (23%). Aortic diameter in women with TS and bicuspid aortic valve was significantly larger than in TS with tricuspid valves in both the ascending (32.4 +/- 6.7 vs. 26.0 +/- 4.4 mm; p < 0.001) and descending (21.4 +/- 3.5 vs. 18.8 +/- 2.4 mm; p < 0.001) aorta. Aortic diameter correlated to age (R = 0.2 - 0.5; p < 0.01), blood pressure (R = 0.4; p < 0.05), a history of coarctation (R = 0.3; p = 0.01) and bicuspid aortic valve (R = 0.2-0.5; p < 0.05). Body surface area only correlated with descending aortic diameter (R = 0.23; p = 0.024).

Conclusions: Aortic dilatation was present in 23% of adult TS women, where aortic valve morphology, age and blood pressure were major determinants of the aortic diameter.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Aorta, Thoracic / pathology*
  • Aorta, Thoracic / physiopathology
  • Aortic Coarctation / complications
  • Aortic Diseases / diagnosis*
  • Aortic Diseases / etiology
  • Aortic Diseases / physiopathology
  • Aortic Valve / abnormalities*
  • Aortic Valve / physiopathology
  • Blood Pressure Monitoring, Ambulatory
  • Blood Pressure*
  • Body Surface Area
  • Case-Control Studies
  • Chi-Square Distribution
  • Cross-Sectional Studies
  • Dilatation, Pathologic
  • Echocardiography
  • Female
  • Heart Defects, Congenital / complications*
  • Heart Defects, Congenital / physiopathology
  • Humans
  • Linear Models
  • Magnetic Resonance Imaging*
  • Middle Aged
  • Risk Assessment
  • Risk Factors
  • Turner Syndrome / complications*
  • Turner Syndrome / physiopathology
  • Young Adult