The spectrum of cardiovascular disease in the Marfan syndrome: a clinico-morphologic study of 18 necropsy patients and comparison to 151 previously reported necropsy patients

Am Heart J. 1982 Jul;104(1):115-35. doi: 10.1016/0002-8703(82)90650-0.
No abstract available

Publication types

  • Comparative Study
  • Review

MeSH terms

  • Adolescent
  • Adult
  • Aorta / physiopathology
  • Aorta, Abdominal / physiopathology
  • Aorta, Thoracic / physiopathology
  • Aortic Aneurysm / complications
  • Aortic Aneurysm / pathology
  • Aortic Dissection / complications
  • Aortic Dissection / pathology
  • Aortic Rupture / complications
  • Aortic Rupture / mortality
  • Aortic Rupture / pathology
  • Aortic Valve Insufficiency / complications
  • Aortic Valve Insufficiency / pathology
  • Cardiovascular Diseases / complications*
  • Cardiovascular Diseases / pathology
  • Endocarditis, Bacterial / complications
  • Endocarditis, Bacterial / etiology
  • Endocarditis, Bacterial / pathology
  • Female
  • Heart Failure / complications
  • Heart Failure / mortality
  • Heart Failure / pathology
  • Humans
  • Hypertension / complications
  • Hypertension / pathology
  • Male
  • Marfan Syndrome / complications*
  • Marfan Syndrome / pathology
  • Middle Aged
  • Mitral Valve Insufficiency / complications
  • Mitral Valve Insufficiency / etiology
  • Mitral Valve Insufficiency / pathology
  • Necrosis
  • Pain / complications
  • Pain / pathology
  • Thorax / physiopathology