An isolated, long segment abdominal aortic coarctation is an infrequent occurrence. Although different names have been given to this entity, it is believed that all represent different stages of nonspecific inflammatory arteritis, or Takayasu's disease. Usually involving the arch and descending aorta, occasionally an isolated segment of the abdominal aorta is involved. Morbid presentation reflects the involvement with narrowing of visceral branches and aortic occlusive disease, as illustrated in this case. Operative intervention with aortic bypass and visceral revascularization is the treatment of choice for recurrent or extensive aortic involvement.