The amyloidoses are a group of diseases in which amyloid, a proteinaceous substance,
deposits in one or more organs. As many as 23 different precursor proteins to the formation …

Cardiac involvement in patients with amyloidosis is common. It produces significant clinical
symptoms in about 40% of patients with AL amyloidosis. A significant proportion of patients …

The symptoms and signs of heart failure can occur in the setting of an increased cardiac
output and has been termed 'high output heart failure'. An elevated cardiac output with …

We reviewed clinical presentation, investigations, therapy, prognosis and outcome of 232
patients with primary (AL) cardiac amyloidosis. There were 142 men and 90 women. Median …

AL (amyloid light-chain) amyloidosis is an uncommon plasma cell disorder in which
depositions of amyloid light-chain protein cause progressive organ failure and death in a …

OBJECTIVE: To determine whether patients with myocardial amyloidosis due either to AL
(primary) amyloid or familial amyloid have distinguishing echocardiographic or …

The morbidity and lethality of AL amyloidosis is caused by the deposition of lg light chains as
fibrillar amyloid protein in vital organs, disrupting their function, and not by the generally low …

Aims Heart failure chiefly affects the elderly, with frequent emergency admissions.
Telemonitoring can identify worsening heart failure but previous randomized trials have …

BACKGROUND: Heart transplantation (TX) for cardiac amyloidosis is uncommon because of
concern about progression of amyloid in other organs and the possibility of amyloid …

Objectives. This study sought to determine the spectrum of electrophysiologic abnormalities
found in patients with cardiac involvement due to AL (primary) amyloidosis and to evaluate …